Selected article for: "acute intermittent porphyria and intermittent porphyria"

Title: Research Communications of the 24th ECVIM-CA Congress
  • Document date: 2015_1_10
  • ID: r59usk02_139
    Snippet: Urinary d-aminolevulinic acid, porphobilinogen, uroporphyrin I, and coproporphyrin I concentrations were increased in the cat studied, suggesting an acute intermittent porphyria (AIP). The erythrocytic hydroxymethylbilane synthase (HMBS) activity in erythrocytes was approximately half normal suggesting a dominant enzymopathy, while the erythrocyte uroporphyrinogen IIIsynthase activity was normal. Sequencing the feline HMBS gene revealed a heteroz.....
    Document: Urinary d-aminolevulinic acid, porphobilinogen, uroporphyrin I, and coproporphyrin I concentrations were increased in the cat studied, suggesting an acute intermittent porphyria (AIP). The erythrocytic hydroxymethylbilane synthase (HMBS) activity in erythrocytes was approximately half normal suggesting a dominant enzymopathy, while the erythrocyte uroporphyrinogen IIIsynthase activity was normal. Sequencing the feline HMBS gene revealed a heterozygous intronic 12 base deletion (c.772-13_-2del) which results in an insertion in the mRNA and would predict a truncated protein.

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